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Macular Telangiectasia Type 2 (Idiopathic Perifoveal Telangiectasia, Idiopathic Juxtafoveal Telangiectasis Type 2)

Macular telangiectasia type 2 has also been termed idiopathic perifoveal telangiectasia or idiopathic juxtafoveal telangiectasis type 2. It is now referred to as Mactel type 2, and it is a bilateral perifoveal vasculopathy which originates in the deep retinal capillary plexus in the temporal juxtafoveal region. As it progresses, it involves the superficial retinal capillary plexus, and continues to progress anteriorly, posteriorly, and circumferentially. This is called the non-proliferative stage of the disease. Mactel type 2 becomes proliferative when the vasogenic process extends under the retina, forming detachment and a retinal–retinal anastomosis. This form of the disease may eventually lead to disciform scarring.

Fundus Autofluorescence

Fundus autofluorescence is used to detect the earliest stages of Mactel type 2 and is useful for family members of patients who may be …